I have been researching pulmonary fibrosis in scleroderma. I have found out some encouraging information regarding pulmonary fibrosis in people with Scleroderma, I am talking about Interstitial lung disease and scleroderma.
If you research it, do not read about “idiopathic pulmonary fibrosis.” This is completely different lung disease and has a very poor survival rate.
People with scleroderma and lung disease can have lung involvement and live for many years, unlike idiopathic pulmonary fibrosis (IPF).
So if you have lung disease and scleroderma, only research it in patients with Interstitial lung disease with scleroderma.
Lung disease is still the leading cause of death in scleroderma. But remember its not as bad in many cases like idiopathic pulmonary fibrosis.
I only touched on Interstitial lung disease, and not pulmonary arterial hypertension. I don’t know if I have that, will know more when I get my echocardiogram.
I have Interstitial lung disease, and its test outcome was moderately restricted defect, according to a PFT back in Jan 2013. I am not so worried now as I was before. Educate yourself, but don't self diagnose.