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Types of Scleroderma Video Presented by Isabella Ensz
There are many methods used to categorize the various forms of scleroderma, which has brought about a confusing abundance of terms.
The following categories are often found in patient literature, but use and interpretation of these categories varies quite a bit. (Also see: What is Scleroderma?)
The systemic forms can affect any part of the body (skin, blood vessels, and internal organs.) The systemic forms are also referred to as "systemic sclerosis" plus other terms such as diffuse, limited, CREST, and overlap.
The localized forms are morphea and linear. They affect only the skin (and sometimes the underlying tissues) but do not affect the internal organs, or reduce one's life expectancy in any way.
When any form of scleroderma (either localized or systemic) occurs in children, it is also called Childhood Scleroderma or Juvenile Scleroderma.
Determining the Type of Scleroderma
Profile of Pre-Scleroderma Evolution. All those patients who evolved to SSc presented the following at baseline: Raynaud's, positive anti-Scl-70 or anticentromere, sclerodactyly or visceral (esophageal) involvement and slow capillaroscopic pattern of scleroderma. E. Delgado. (THU0323) EULAR 2009.
Juvenile Scleroderma. When any form of scleroderma (either localized or systemic) occurs in children, it is also called Childhood Scleroderma or Juvenile Scleroderma. ISN.
Localized Scleroderma.There are two types of localized scleroderma: linear and morphea. Localized scleroderma affects the skin. It may also affect the underlying muscles and bones, but it does not affect internal organs, and it does not reduce a person's life expectancy. ISN.
Systemic scleroderma is also known as systemic sclerosis (SSc). There are several types, Limited/CREST and Diffuse. These types can affect the entire body, including the skin, blood vessels, and/or internal organs. ISN.
Systemic Sclerosis (Scleroderma): Prognosis and Mortality. Now that the full range of types and severity of scleroderma are being recognized and diagnosed, there is increasing awareness that many people have a milder type of illness with a much rosier longterm prognosis. ISN.
