| Localized
Scleroderma: Linear |
| This page
was written by Shelley
Ensz, and medically edited by Dolores Vázquez-Abad,
M.D.. The sections on En Coup de Sabre and Parry-Rombergs have
not been medically edited yet. See Disclaimer. |
|
| What is Linear Scleroderma? |
| Linear Scleroderma is a line of
thickened skin which can affect the bones and muscles underneath
it, thus limiting the motion of the affected joints and muscles.
It most often occurs in the arms, legs, or forehead, and may
occur in more than one area. |
| Its most likely to be on just one
side of the body. Linear Scleroderma generally appears
in young children, and is characterized by the failure of one
arm or leg to grow as rapidly as its counterpart. |
| Systemic Sclerosis and Localized Scleroderma in Childhood. Juvenile scleroderma syndromes, including the systemic and the localized varieties, represent the third most frequent chronic rheumatic conditions in pediatric rheumatology practice. (ScienceDirect) Rheumatic Disease Clinics of North America Vol 34, Issue 1, Feb 2008, Pp 239-255. (Also see: Juvenile Scleroderma) |
| Generalized Linear Scleroderma in Childhood. A 6 year-old girl presented with linear hyperpigmented, indurated plaques on the upper and lower extremities of 9 months duration The onset followed a febrile illness that was diagnosed as typhoid. Dermatology Online Journal 13 (3): 34. 2007. (Also see: Juvenile Scleroderma) |
| Congenital
localized scleroderma (CLS). CLS is a rare and probably
underestimated condition in neonates. CLS should be included
in the differential diagnosis of infants with cutaneous erythematous
fibrotic lesions to avoid functional and aesthetic sequelae
and to allow prompt therapy. PubMed. J Pediatr. 2006 Aug;149(2):248-51.
(Also see: Juvenile
Scleroderma) |
| Localized
scleroderma is an autoimmune disorder. Many previous
studies conclude that localized scleroderma involves autoimmune
abnormalities and is one of the organ-specific autoimmune
disorders targeting mainly skin, although the types of autoimmune
abnormality are different from systemic sclerosis. PubMed.
Rheumatology (Oxford). 2004 Nov 23. (Also see: Types
of Scleroderma: Localized, Morphea and Dr.
Shinichi Sato) |
| Unilateral
generalized morphea (UGM) is a rare variant of localized
scleroderma. As the onset of UGM usually occurs in pediatric
patients, pediatricians should be cognizant of the presentation
of this uncommon condition. PubMed. Eur J Med Res. 2006
Apr 28;11(4):152-6. (Also see: Localized Scleroderma: Morphea and Juvenile
Scleroderma) |
| Is
Juvenile Localized Scleroderma really "LOCALIZED"? One
fourth of JLS patients in this data series presented various
kind of extra-cutaneous manifestations, sometimes with multiorgan
involvement. For this reason, the term "localized" is
somehow inappropriate. These findings should change our clinical
approach to this disease and underline the need for systemic
immunosuppressive treatment for some patients. Francesco
Zulian. ACR Conference Oct. 2003. (Also see: Types
of Scleroderma and Morphea) |
| Juvenile
localized scleroderma in the first year of life. JLS
can start as early as during the first year of life and can
be present even at birth. Linear subtype was the prevalent
manifestation of the disease. Since the diagnostic delay
was remarkable and the evolution quite aggressive, JLS should
be considered in the differential diagnosis of infants with
fibrotic or hyperpigmented skin lesions. Francesco Zulian.
1396/218. ACR 2004. |
| Localized
scleroderma in adults and children. Clinical and laboratory
investigations on 239 cases. Children and adults developed
LS with analogous clinical and immunological features. However,
the prevalence of LS variants differed between adult and
pediatric populations, leading to different extracutaneous
complications. Among adults, Raynaud's phenomenon
was found in 8 patients; interestingly, anticentromere
antibodies were detected in 4 of these subjects, identifying
a subset at risk for progression to systemic
disease. PubMed. Eur J Dermatol 2003 Mar-Apr;13(2):171-6.(Also
see: Morphea) |
| Circumscribed
scleroderma belongs to the groups of the diseases characterized
by fibrosis of the skin and the deeper tissue. PubMed.
Przegl Lek 2002;59(11):898-902. (Also see: Morphea) |
| Linear
Scleroderma and Autoimmune Hemolytic Anaemia We describe
an association wherein linear scleroderma coexisted with
autoimmune haemolytic anaemia. J Assoc Physicians India
2002;50:441-442. |
| Scleroderma:
a case report of possible cause of restricted movement of
the temporomandibular joint with effects on facial development. Localized
scleroderma is often benign, but may cause significant deformity,
if it occurs on the face or extends across joint surfaces.
Structural changes may occur in the osseous tissue and result
in mandibular joint restriction (pseudoankylosis) and facial
and occlusal disharmonies. PubMed. J Clin Pediatr Dent.
2003 Fall;28(1):33-8. (Also see: Morphea and Dental
Involvement) |
| Linear
scleroderma along blaschko's lines in a patient with systematized
morphea. Since both the unilateral distribution and the
lesions along Blaschko's lines are the patterns created by
genetic mosaicism, we suggest that a significant part of
linear scleroderma and perhaps a smaller part of multiple
morphea could be related to cutaneous mosaicism. PubMed.
Acta Derm Venereol. 2003;83(5):362-4. (Also see: Morphea) |
| En Coup de Sabre |
| Linear Scleroderma can appear as
a long streak resembling a deep sabre wound — often called "en
coup de sabre." NIH. |
| En Coup de Sabre is a rare, sporadic
disease of indeterminate etiology which is characterized by
progressive atrophy and deformity of one side of the face.
Seizure disorder is another feature of this disease." Neuroradiology
Reading Room V 2.0, Mayo Foundation. |
|
| Parry-Rombergs Syndrome |
| Parry-Rombergs
Syndrome, is also known as Progressive Hemifacial Atrophy
or HFA. This may be the same as Linear Scleroderma affecting
the facial area. |
| En
coup de sabre morphea and Parry-Romberg syndrome: a retrospective
review of 54 patients. En coup de sabre morphea and Parry-Romberg
syndrome frequently coexist and are likely both variants
of morphea. Bilateral disease is more common than previously
reported. The efficacy of antimalarials and methotrexate
in the treatment of these diseases remains unclear. PubMed.
J Am Acad Dermatol. 2007 Feb;56(2):257-63. (Also see: En
Coup de Sabre) |
| Neuroretinitis,
Parry-Romberg syndrome, and scleroderma. The authors
report a new case of progressive hemifacial atrophy (Parry-Romberg
syndrome). They emphasize the rarity of this disease, its
etiology, which remains controversial, the diversity of its
ophthalmologic manifestations, and its relations with scleroderma
and autonomic nervous system disorders are discussed. Acute
neuroretinitis remains rare and its pathogeny is unknown. PubMed.
J Fr Ophtalmol. 2005 Oct;28(8):866-70. |
| Beneficial
effect of immunosuppressive drugs on Parry-Romberg syndrome. We
observed beneficial effects of immunosuppressive agents on
neurologic lesions in particular in a patient with PRS who
presented with immunoinflammatory findings and neurologic
involvement, apart from cutaneous manifestations. PubMed.
South Med J. 2005 Sep;98(9):940-2. |
| Progressive
hemifacial atrophy with linear scleroderma. We think
that linear scleroderma of childhood and hemifacial atrophy
have considerable clinical overlap and these two syndromes
appear to be manifestations of the same or related pathogenic
processes. Recently, the beneficial effects of 1.25-dihydroxyvitamin
D3 (calcitriol) were reported in adults and in children with
linear scleroderma. Our result indicates that calcitriol
may be an effective agent for treating localized scleroderma
in children. PubMed. Pediatr Dermatol. 2005 Sep-Oct;22(5):436-9. |
| Progressive
visual loss in a child with Parry-Romberg syndrome. We
present a young girl originally felt to have linear scleroderma
and anisometropic amblyopia, who was eventually diagnosed
with Parry-Romberg syndrome as the cause of her cutaneous
and ophthalmologic findings. PubMed. Semin Ophthalmol.
2004;19(3-4):91-4. |
| Facial
hemiatrophy--a report of 5 cases. Progressive hemifacial
atrophy (Parry Romberg Syndrome) is usually sporadic but
a few familial cases have been reported suggesting a possible
hereditary influence and many investigators believe it to
be a localized form of scleroderma. PubMed. Indian J Dent
Res. 2003 Oct-Dec;14(4):238-45. |
| Parry-Romberg
syndrome: A possible association with borreliosis. This
syndrome has many features of linear scleroderma 'en coup
de sabre' but is distinguished by more extensive involvement
of the lower face with only slight cutaneous sclerosis. A
case of progressive hemifacial atrophy occurring in a 30-year-old
woman is reported, in which the aetiology is thought to be
Lyme disease, a borrelial infection. PubMed. J Eur Acad
Dermatol Venereol. 2004 Mar;18(2):204-207. (Also see: Causes
of Scleroderma: Infection) |
| Parry-Romberg
syndrome: A global survey of 205 patients using the Internet. Parry-Romberg
syndrome (PRS) is a rare neurocutaneous disorder characterized
by progressive facial hemiatrophy. There was a wide range
of age at onset and considerable diagnostic overlap with
scleroderma "en coup de sabre." PubMed. Neurology.
2003 Sep 9;61(5):674-6. |
| Sclerodermic Linear
Lupus Panniculitis |
| Sclerodermic
linear lupus panniculitis: report of two cases. Lupus
erythematosus panniculitis is a rare disease characterized
by deep subcutaneous nodules, most commonly localized on
the upper limbs and face. We present here the clinical characteristics,
course and laboratory findings of 2 patients having linear
lupus erythematosus panniculitis with localized scleroderma-like
changes. PubMed. Dermatology. 2005;210(4):329-32. (Also
see: Lupus, Linear
Scleroderma, and Overlap
Syndrome) |
| Diagnosis |
| Linear scleroderma is usually diagnosed
by clinical examination. It is often confirmed by skin biopsy.
Skin biopsies are usually a very tiny sample of tissue and
the procedure is often very quick, easy and with minimal discomfort.
Ultrasound has also been found to be useful for the diagnosis
of Localized Scleroderma (such as linear). |
| Localized Scleroderma (LS) Severity Index and Global Assessments: A Pilot Study of Outcome Instruments. LS clinical trials are impeded by the lack of reliable and reproducible outcome measures. We have developed the LS Severity Index (LoSSI) to correct this deficiency. Journal of Rheumatology. Volume 35: No. 3 March 2008. |
| Plaque-type
scleroderma associated with linear and oesophageal features and
facial and extra-facial hemiatrophy. The combination of several
sub-types of scleroderma and facial and extra-facial hemiatrophy
in the same patient may indicate that these entities actually
represent different spectra of the same disease. PubMed. Ann
Dermatol Venereol. 2007 Jan;134(1):68-71. (Also see: Morphea) |
| A
new computerized method for the assessment of skin lesions
in localized scleroderma (LS). CSS (computerized skin
score) has shown to be a reliable method to assess the skin
lesions in patients with LS. It is reproducible, easy to
use and, with the support of the CSS software, applicable
worldwide. PubMed. Rheumatology (Oxford). 2007 Jan 30.
(Also see: Localized
Scleroderma: Morphea) |
| Ultrasonography
(USG) is a Sensitive Tool for Monitoring Localized Scleroderma
(LS). Changes seen on USG correlated with assessed clinical
changes, both improvement and worsening. Using USG to monitor
patients with LS may, therefore, be useful for guiding treatment
strategies and as a tool in controlled clinical trials. Suzanne
C. Li. 1699/370 ACR 2006. |
| Serum
Autoantibodies and their Clinical Associations in Patients
with Childhood and Adult Onset Linear Scleroderma. Childhood
onset Linear Scleroderma is similar to adult onset disease
in regard to the frequency of serum autoantibodies. Thaschawee
Arkachaisri. 289/289 ACR 2006. (Also see: Antibodies) |
| Serum
Autoantibodies and their Clinical Associations in Patients
with Childhood and Adult Onset Linear Scleroderma (LScl). Childhood
onset LScl is similar to adult onset disease in regard to
the frequency of serum aAbs. Over two thirds of LScl patients
had ANA. Thaschawee Arkachaisri. 289/289 ACR 2006. (Also
see: Antibodies) |
| Antihistone
antibodies (AHAs) in linear scleroderma variants. AHAs,
which traditionally are markers for drug-induced lupus, may
also be linked to linear scleroderma. The AHA titers may
be related to the extent of involvement as well as disease
activity. PubMed. Int J Dermatol. 2006 Nov;45(11):1296-9.
(Also see: Antibodies) |
| Rheumatoid
factor isotypes in localized scleroderma. The presence
of RF isotypes is one of the immunological abnormalities
of localized scleroderma. IgM RF seemed to be most useful
of these three factors to determine the severity of disease. PubMed.
Clin Exp Dermatol. 2005 Jul;30(4):405-8. |
| Thirteen-megahertz
ultrasound probe: its role in diagnosing localized scleroderma. Ultrasound
imaging has been shown to be useful for the evaluation of
systemic and localized scleroderma (LS). However, its specificity
and sensitivity have not been studied. Conclusions Thirteen-megahertz
ultrasound is a valuable tool for diagnosing LS. Morphological
ultrasound diagnostic criteria had a high specificity and
a high sensitivity. PubMed. Br J Dermatol 2003 Apr;148(4):724-9
(Also see: Morphea ) |
| TNF
and IL-13: Serum levels of tumor necrosis factor and interleukin-13
are elevated in patients with localized scleroderma. These
results suggest that TNF and IL-13 may be associated with
the development of LSc. PubMed. Dermatology. 2003;207(2):141-7.
(Also see: Morphea and Antibodies) |
| Anti-DNA
Topoisomerase II Alpha Autoantibodies in Localized Scleroderma. The
present results indicate that anti-topo II alpha Ab is a
major autoantibody in LSc, which is distinct from anti-topo
I Ab in SSc. Furthermore, our results suggest that the high
prevalence of anti-topo II alpha Ab in LSc and exclusive
presence of anti-topo I Ab in SSc suggest that Abs to enzymes
of the topoisomerase family are associated with fibrotic
disorders including LSc and SSc. Ikuko Hayakawa. ACR Conference
Oct. 2003 (Also see: Localized
Scleroderma: Morphea and Antibodies) |
| Treatment |
| No treatment, medication or ointment
has been proven by large-scale placebo-controlled studies to
alter the course of Linear Scleroderma. A placebo-controlled
study is still necessary to confirm the methotrexate/corticosteriod
therapy; and, by any means, these are toxic therapies, particularly
in children. |
| Pulsed
high-dose corticosteroids combined with low-dose methotrexate
in severe localized scleroderma. These data suggest that
pulsed high-dose corticosteroids combined with orally administered
low-dose methotrexate therapy is beneficial and safe in the
treatment of patients with LS. This treatment regimen should
especially be considered for severe forms of LS in which
conventional treatments have failed. PubMed. Arch Dermatol.
2005 Jul;141(7):847-52. (Also see: Morphea) |
| Photodynamic
therapy (PDT) in dermatology. A therapeutical benefit
of PDT is also evident for inflammatory dermatoses like localized
scleroderma, acne vulgaris and granuloma annulare. The benefits
of PDT are the low level of invasiveness and the excellent
cosmetic results after treatment. PubMed. Photodermatol
Photoimmunol Photomed. 2005 Jun;21(3):142-9. (Also see: Morphea) |
| Phototherapy
and photochemotherapy of sclerosing skin diseases. Two
phototherapeutic modalitites are used for the treatment of
sclerosing skin diseases, long-wave ultraviolet A and psoralen
plus ultraviolet A (PUVA). PubMed. Photodermatol Photoimmunol
Photomed. 2005 Jun;21(3):157-65. |
| Good
News for Children with Localized Scleroderma According
to the July-August 2000 issue of "Arthritis Today" (p.30), "Localized
scleroderma (LS) in children can be treated easily and its
disfiguring effects minimized with appropriate therapy. A
new Canadian study suggests the best therapy for the arthritis-related
disease, which damages areas of skin and underlying tissue,
is a course of methotrexate in combination with glucocorticoids.
So far, most of the cases researchers have treated with this
regimen have gone into remission. |
| Topical
tacrolimus in the treatment of localized scleroderma. These
were the first cases of successful topical tacrolimus therapy
in localized scleroderma and should be regarded as a promising
treatment option for LS, especially on account of its high
tolerability that permits prolonged use without side-effects. PubMed.
Eur J Dermatol. 2003 Nov-Dec; 13(6): 590-2. (Also see: Morphea) |
| Ultraviolet
A1 phototherapy. Another condition for which UVA1 is
effective, and is particularly promising because we have
no reliably effective treatment already, is localized scleroderma. PubMed.
Br J Dermatol 2003 Apr;148(4):626-37 (Also see: Scleroderma
Treatments and Morphea) |
| Linear Patient and Caregiver Stories |
| AJ
Miller: Linear Scleroderma I
have had Linear Scleroderma since 1968, when I was 7 years
old. I have never met anyone else with it... |
| Alicia:
Linear Scleroderma My doctor said the people who are
looking at me and seeing the scars are the ones who need
healing, and that I should pray for them... |
| Alicia
B: Localized Morphea with possible Parry Romberg Syndrome The
doctor kept saying something had eaten away at all the fatty
tissue and the muscles which left it just skin, blood, bone,
and nerve so when you look at it, it looks like I have dirt
on my face and a gaping hole to go with it... |
| Angel:
Linear Scleroderma I have linear scleroderma. I have
had it for a little over five years and I am only twelve... |
| Angela:
Mother of Linear Scleroderma Patient We are in search
of others who know how to handle the pain and muscle spasms
in her legs... |
| Anna:
Linear Scleroderma (Poland) I realised that it is
not worthwhile to give up, even during the most difficult
moments; it is necessary to fight and to believe that it
will be better. If I had not believed I would not have been
alive now... |
| Ariel:
Linear Morphea Luckily, it only affects my skin, so
I can still dance and play the piano... |
| Ariel
M-S: Linear Morphea Within six months, the morphea
had eaten away almost all of the fat on my arm and I have
developed nerve and muscle pains that do not go away... |
| Ashlin:
Localized Scleroderma It took me five months to realize
that I needed to go to the doctor, and now I feel that I
should not have waited so long... |
| Aurora:
Linear Scleroderma I am always very tired, and I suffer
from pain that will not go away no matter what I do... |
| (Español/Spanish)
Aurora: Esclerodermia Lineal Estoy agotada continuamente,
y padezco dolores que no se quita con nada... |
| Carolina:
Linear Scleroderma As time went by it disseminated
throughout my leg and reached my foot... |
| (Español/Spanish)
Carolina: Esclerodermia Lineal Luego de multiples
examenes, de reiteradas visitas a diferentes dermatólogos
e inmunólogos diagnosticaron una escleroderma localizada
de tipo lineal... |
| Catherine:
Mother of Linear Scleroderma Patient Emma's linear
scleroderma started on her left cheek at the age of 4 years
and by the time she was eight that side of her face was quite
deformed... |
| Charmaine
C: Lichen Sclerosus and Scleroderma Soon multiple
spots developed across my abdomen, with a few stray ones
on my forearms and more on the left leg... |
| Chris
S: Mother of Linear Morphea Patient Whatever it was,
I knew it should not be there... |
| Christin:
Linear Scleroderma My name is Christin. I am a twenty-year-old
college student. I have had scleroderma for as long as I
can remember... |
| Davie's
Mom: Mother of Linear Scleroderma Patient Davie could
be a candidate for skin grafts. If anyone has tried this
I would love some input... |
| Debbie
W: Mother of Linear Scleroderma Patient Because my
daughter's face was being affected so severely with atrophy,
hair loss, and partial loss of her eyebrow we began a treatment
program... |
| Debra
R: Mother of Emma, Linear Scleroderma Patient It is
so good to have support and be able to ask questions and
have them answered. Now I can explain to Emma what is going
on... |
| Deedra:
Linear Scleroderma In the course of two years the
scleroderma spread from under my knee to the top of my thigh... |
| Desiraye:
Linear Morphea When I was 14 years old, I spent the
whole summer laying out in the sun. I developed a white patch
that my mother thought was ringworm... |
| (Polski)
Dorota: Twardzina linijna (coup de sabre) Moja historia
z twardzina zaczela sie 15 lat temu i do dzisiaj (kiedy trafilam
na strony serwisu o sklerodermii) nie zdawalam sobie sprawy
z tego, jak powazna... |
| Ed:
Father of a Linear Morphea Patient A series of medications,
steroids and creams has been applied, but Erwin's case seemed
to be worsening... |
| Edna
S: Linear Scleroderma I am desperate because I know
this is a deteriorating illness... |
| Emmi:
Linear Scleroderma and Vitiligo My parents thought
I was going to die, and doctors here in Finland did not really
know what to do with me. There are not many scleroderma cases
in Finland... |
| (Español/Spanish)
Edna S: Esclerodermia Lineal Estoy desesperada por
que sé que esto es una enfermedad deteriorante... |
| Erica:
Mother of Daughter with Linear/Morphea Scleroderma She
went there with one spot and now she has them all over both
arms, one hand, her back, knee and thigh... |
| (Italiano)
Eugenio: Sclerodermia Lineare lPremetto che mi rendo
conto della difficoltà di rispondere ad una mail senza
poter vedere il paziente ma, come padre, ho sentito il bisogno
di scriverLe per sapere la Sua opinione... |
| Gina:
Morphea or Linear Scleroderma I really try to put
it out of my mind and be thankful that it is not systemic.
But, every time I notice new areas turning color it really
worries me... |
| Ginger: Generalized/Linear Scleroderma After analyzing all the test results and my medical records the neurologist
attributed the muscle atrophy to the linear scleroderma... |
| Heather: Vitiligo, Hypothyroidism, and now Linear Morphea I am not too concerned about
the other two conditions since there really is nothing you can do about
the vitiligo, and the
thyroid is under control. The morphea is what is bugging me... |
| Hope:
Linear Morphea My mom took me to the doctor and for
three months he treated it as ringworm... |
| Jan
L: Linear Scleroderma and Vitiligo I was not ever
overly concerned with my looks, so I really did not pay that
much attention to it... |
| Jason:
Linear Scleroderma I have recently been diagnosed
with Raynaud's as well, have had gastro-intestinal difficulties
more common to systemic forms, and have witnessed these lesions
grow and deepen rather than decrease in size... |
| Jennifer M: Mom of Linear Morphea Patient Almost the minute that the doctor walked into the room she knew what it was. The first words out of her mouth were, "That's linear morphea"... |
| (Español/Spanish)
Jessica: Madre de Paciente con Esclerodermia Localizada en
Golpe de Sable Tengo una niña de 6 años
de edad, le diagnosticaron Esclerodermia Lineal en golpe
de sable desde los 3 años... |
| Jessica
M.: Mother of Linear Morphea Patient About eight months
ago my daughter developed a dark circle on her leg. It looked
like a deep bruise, but we let it go. It never went away... |
| Judy
C: Mother of a Daughter with Linear Morphea Scleroderma Three
months ago, our oldest daughter, Alison, was diagnosed with
Linear Morphea Scleroderma (Juvenile Scleroderma)... |
| Julie
B: Mother of Linear/Morphea Scleroderma Patient Her
right leg is badly affected with a lot of scarring and muscle
wasting and also the leg length... |
| Kathy
Gaither: Mother of Juvenile Scleroderma Patient I
decided that I was going to turn our negative experience
with scleroderma into something positive for us and for other
parents... |
| (Dutch)
Leon: Lineair Bij mij ontdekte men op 5 jarige leeftijd
twee vlekjes op mijn linker onderarm... |
| Lancia:
A Friend of a Morphea Patient (Italy) Some time ago
a beloved friend of mine was diagnosed with scleroderma... |
| Lisa
Kate McGowan: Linear Scleroderma When I was eighteen
years old, I was diagnosed with linear scleroderma. It changed
my life because it affected my left arm by leaving a big
shiny scar... |
| Louise:
Linear Scleroderma I got a bit of a fright when I
read about scleroderma affecting the organs... |
| (Italiano)
Lucia: Sclerodermias a Colpo di Sciabola La lesione
c depressa, larga circa un centimetro,di coloro scuro, localizzata
in posizone centrale sulla fronte... |
| Malen:
Linear Scleroderma (Philippines) My symptoms included
severe cramps in my right leg, where the pain is pushing
me to my limits. My leg and arm on the right side of my body
are smaller... |
| Mary
B: Scleroderma En Coup de Sabre I feel like it is
tearing my head open. Sometimes I get headaches, and I believe
it is because of this illness... |
| (Español/Spanish)
Mary B: Esclerodermia en Golpe de Sabre Por el contrario
siento que se me está haciendo una enorme brecha en
la cabeza. A veces me dan dolores de cabeza y creo que es
por causa de esta enfermedad... |
| Maria
R: Linear Scleroderma I am as healthy as I ever was,
except the line on my forehead never disappeared, but it
does not bother me in any way... |
| Martina:
Linear Morphea (Ireland) I am twenty-four years old.
I was diagnosed with linear morphea in September... |
| Mary-Charlotte:
Juvenile Linear Scleroderma I am now fourteen years
old, and I have been in remission for about six years. I
no longer take methotrexate or occupational therapy... |
| Melanie
W: Linear Morphea Scleroderma The only good thing
about this disease is that it makes you a better person.... |
| Miguel:
Linear Scleroderma I am twenty-seven years old and
some months ago I went to see a doctor because I had a spot
on my left leg... |
| (Español)
Miguel: Esclerodermia Lineal Hace unos meses fui a
ver a un médico porque tenía una mancha en
mi pierna derecha, no me molestaba pero mi piel comenzaba
a endurecerse en esa área... |
| (Italiano)
Paola - Sclerodermia Lineare 3 anni fa ho visto sotto
il malleolo del piede destro di mio figlio Giacomo, che allora
aveva 8 anni, una macchia color... |
| Patty
S.:Localized Scleroderma, Pulmonary Hypertension and Sjögren's I
have quit my job and reduced my stress a hundred percent.
I am doting on my children and my husband... |
| Rhea:
Morphea The giant spot on my back started out as Morphea
and then started gaining more qualities of Linear Scleroderma... |
| Rodriguez:
Linear Scleroderma Little by little pigmentation is
coming back into my leg and there are times I still feel
joint pain but I have gotten through it... |
| Rubie: Linear Morphea Scleroderma I was
referred to a dermatologist and was finally diagnosed with linear morphea
at the age of four... |
| Sarah H: Linear Scleroderma When
I was very young, two or three years old, my mom started to notice
that the top of my scalp was changing... |
| Stacie: Linear Scleroderma I may have been incurable at four years old but it gave
me an insight. I appreciate my life so much more than I would have
thought. It could be worse... |
| Tami:
Morphea Scleroderma I have gotten used to the stares
everyone casts my way because in their eyes I am different.
Unique, I guess... |
| Tammy:
Mother of Son with Linear and Morphea Scleroderma Brandan
has linear scleroderma on his right side and morphea on his
chest pretty bad... |
| Tammy
M: Linear Scleroderma and Vitiligo When I was first
diagnosed there was no such thing as the Internet. I always
felt that my family and I were the only ones in the world
who knew what scleroderma was... |
| Terry
E. (Mojoy the Clown): Morphea Profunda Linear Scleroderma My
right lower leg started to swell and the ankle grew big.
It hurt all the time... |
| (Italiano)
Tommaso DM: Lineare Ho quasi 13 anni. Sedici mesi
fa mi è stata diagnosticata la sclerodermia... |
| Tore: Linear Scleroderma However, as time went by, the patch extended, and the hardening, instead of going down, got worse, involving more and more parts of my leg, all the way to my knee... |
| (Italiano) Tore: Lineare La cute
ma anche i tessuti sottocutanei risultavano induriti. In realtà sembrava
che la pelle si fosse completamente attaccata all'osso, dal quale era
impossibile smuoverla... |
| Tori:
Localized Juvenile Scleroderma This is not the first
rare disease that I have had... |
| Vanessa:
Linear Scleroderma My older sister found a way to
cover up the nasty disease on my forehead. Bangs! It was
a great idea... |
| Yally:
Dermatitis with Linear/Morphea My daughter has a spot
on her left leg, that almost covers it completely... |
| (Español/Spanish)
Yally: Dermatitis con Consistencia en Morfea/Lineal Mi
temor siempre ha sido el consumir indefinidamente la droga... |
| See Also |
| Causes
of Scleroderma. ISN. |
| En Coup de Sabre. Includes patient stories. ISN. |
| Juvenile
scleroderma. Scleroderma is a relatively rare disorder
in children. Among its subsets, localized scleroderma is
more common in children than the systemic variety. Curr
Opin Rheumatol 2002 Sep;14(5):553-61 PubMed. |
| Juvenile
Scleroderma. ISN. |
| Parry-Rombergs
Syndrome. Includes patient stories. Parry-Rombergs
Syndrome. |
| Scleroderma
Photos. Pictures of scleroderma symptoms, including
photos of Linear Scleroderma. |
| Submit
your Linear Scleroderma story in any language. ISN. |
