Morphea, Linear, En Coup de Sabre, Parry Rombergs
Patient and Caregiver Stories
There are two types of localized scleroderma: Linear and Morphea. Localized scleroderma affects the skin. It may also affect the underlying muscles and bones, but it does not reduce a person's life expectancy. (Also see What is Scleroderma? and Types of Scleroderma)
In general, localized scleroderma is relatively mild, and may be related to systemic scleroderma only in terms of similar superficial symptoms, such as the appearance of skin biopsy under the microscope.
Linear scleroderma is a line of thickened skin which can affect the bones and muscles underneath it, thus limiting the motion of the affected joints and muscles. It most often occurs in the arms, legs, or forehead, and may occur in more than one area. ISN.
|Video Overview of Linear
En Coup de Sabre
|Parry Rombergs Syndrome
Sclerodermic Linear Lupus Panniculitis
Linear Patient Stories
Morphea scleroderma usually begins as patches of yellowish or ivory-colored rigid, dry skin. These then become hard, slightly depressed, oval-shaped plaques which usually have a whitish or yellowish center surrounded by a pinkish or purplish halo. ISN.
Types of Morphea
Causes of Morphea
Complications of Morphea
Patient and Caregiver Stories
Linear morphea scleroderma. Sometimes "morphea" is used as a generic term for localized scleroderma of any type. Thus, sometimes the term "linear morphea" refers to localized scleroderma of any type (either linear or morphea).
When "linear morphea" is used more literally, it means that there is a mixture of both types — linear and morphea, occurring together in combination.
Prospective study to evaluate the clinical and radiological outcome of patients with scleroderma of the face. Patients with localized scleroderma of the face have a high prevalence of neurological and ophthalmological changes. All cases of localized scleroderma of the face should be thoroughly examined for the presence of systemic changes. Science Direct, June 19 2013. (Also see Eye Involvement, and Neurological Involvement)
Localized Scleroderma: MR (magnetic resonance) Findings and Clinical Features. The purpose of this study was to describe musculoskeletal manifestations seen at magnetic resonance (MR) imaging in patients with localized scleroderma (LS) and to examine the relationship of MR findings to clinical subtypes and clinically suspected musculoskeletal features. Schanz S. (PubMed) Radiology, 2011 Jun 21.
Juvenile scleroderma: experience in one institution. While scleroderma is rare in children, the prognosis of systemic scleroderma (SSc) is poor but better than for adults. The prognosis for LS (localized scleroderma) is usually benign, however, the skin may become progressively indurated and it may not only be a skin disease. No progression from LS to SSc was observed in our study. Lo CY, Asian Pac J Allergy Immunol, 2010 Dec;28(4):279-86. (Also see Juvenile Scleroderma)
Collagen Degradation Products And Elastin In Systemic (SSc) And Localized Scleroderma (lSSc) . Increased markers of collagen and elastin turnover in SSc and LSc reflect the active fibrotic process in the diseases and are accordance with the published data. High elastin levels in psoriasis vulgaris group are rather difficult to explain. R. Becvar FRI0245 EULAR 2008. (Also see Systemic Scleroderma, and Skin Involvement)
Juvenile Scleroderma by ISN.
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