In general, localized scleroderma is relatively mild, and may be related to systemic scleroderma only in terms of similar superficial symptoms, such as the appearance of skin biopsy under the microscope.
Localized Scleroderma: Linear
Linear scleroderma is a line of thickened skin which can affect the bones and muscles underneath it, thus limiting the motion of the affected joints and muscles. It most often occurs in the arms, legs, or forehead, and may occur in more than one area. ISN.
Morphea scleroderma usually begins as patches of yellowish or ivory-colored rigid, dry skin. These then become hard, slightly depressed, oval-shaped plaques which usually have a whitish or yellowish center surrounded by a pinkish or purplish halo. ISN.
Linear morphea scleroderma. Sometimes "morphea" is used as a generic term for localized scleroderma of any type. Thus, sometimes the term "linear morphea" refers to localized scleroderma of any type (either linear or morphea).
When "linear morphea" is used more literally, it means that there is a mixture of both types — linear and morphea, occurring together in combination.
Localized Scleroderma: MR (magnetic resonance) Findings and Clinical Features. The purpose of this study was to describe musculoskeletal manifestations seen at magnetic resonance (MR) imaging in patients with localized scleroderma (LS) and to examine the relationship of MR findings to clinical subtypes and clinically suspected musculoskeletal features. Schanz S. (PubMed) Radiology, 2011 Jun 21.
Juvenile scleroderma: experience in one institution. While scleroderma is rare in children, the prognosis of systemic scleroderma (SSc) is poor but better than for adults. The prognosis for LS (localized scleroderma) is usually benign, however, the skin may become progressively indurated and it may not only be a skin disease. No progression from LS to SSc was observed in our study. Lo CY, Asian Pac J Allergy Immunol, 2010 Dec;28(4):279-86. (Also see: Juvenile Scleroderma)
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