Prognosis: Localized (Linear/Morphea)
|Prognosis: Systemic (Diffuse/Limited)|
When any form of scleroderma (either localized or systemic) occurs in children, it is also called Childhood Scleroderma or Juvenile Scleroderma. (Also see What is Scleroderma? and Types of Scleroderma)
Localized scleroderma, such as linear, morphea, en coup de sabre, may cause disfigurement and disability (which is why it is important to seek expert care early on). However, localized scleroderma does not reduce a person's life expectancy. (Also see Juvenile Scleroderma Experts)
Juvenile scleroderma: experience in one institution. While scleroderma is rare in children, the prognosis of systemic scleroderma (SSc) is poor but better than for adults. The prognosis for LS (localized scleroderma) is usually benign, however, the skin may become progressively indurated and it may not only be a skin disease. No progression from LS to SSc was observed in our study. Lo CY, Asian Pac J Allergy Immunol, 2010 Dec;28(4):279-86. (Also see Localized Scleroderma)
Systemic sclerosis (scleroderma), such as diffuse or limited/CREST, can affect the skin, blood vessels, and internal organs. In general, the survival rate is better for those who have childhood onset of systemic scleroderma (as opposed to those with adult onset) because children tend to have less internal organ involvement. (Also see Juvenile Scleroderma Experts, Systemic Sclerosis, Systemic Sclerosis Prognosis, and Systemic Symptoms)
Mortality rates for pediatric rheumatology patients significantly lower than previously reported. A recent study by researchers from the Cleveland Clinic found that the overall mortality rate in the U.S. for all pediatric patients with rheumatic diseases was not worse than the age and sex-adjusted population. Furthermore, mortality rates were significantly lower than reported in previous studies of rheumatic diseases and conditions that are associated with increased mortality. E!ScienceNews. January 28, 2010.
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